sturge weber syndrome

Sturge Weber Syndorme is a neurocutaneous syndrome with a facial nevus and angiomas involving the leptomeninges. Glaucoma may or may not be present.
It occurs because of a failure of regression of embryonal blood vessels around the cephalic portion of the neural tube
Neurological dysfunction occurs because of hypoxia, infarction, ischemia, venous occlusion and vasomotor phenomenon in the leptomeningeal angiomas.
Port wine stain in the V1 area of the trigeminal nerve is most likely to have SWS.
Seizures ocur in 75-90%. Glaucoma occurs only if the eyelid is involved.
The port wine stain can be treated with laser therapy.